Journal of Postgraduate Medicine, Education and Research

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VOLUME 53 , ISSUE 1 ( January-March, 2019 ) > List of Articles

CASE REPORT

An Extremely Unusual Case of Type A Interrupted Aortic Arch in a Young Male

Uma Debi, Prem Kumar, Manphool Singhal, Manoj Rohit

Keywords : Aorta, Aortic arch, Coarctation, Interrupted,Angiogram

Citation Information : Debi U, Kumar P, Singhal M, Rohit M. An Extremely Unusual Case of Type A Interrupted Aortic Arch in a Young Male. J Postgrad Med Edu Res 2019; 53 (1):31-33.

DOI: 10.5005/jp-journals-10028-1308

License: CC BY-NC 4.0

Published Online: 00-03-2019

Copyright Statement:  Copyright © 2019; Jaypee Brothers Medical Publishers (P) Ltd.


Abstract

ABSTRACT A young male patient of 20-year-old came to our hospital for evaluation of hypertension in young. The patient has presented with symptoms of dizziness and heaviness of the head for past 3 months. ECHO was suggestive of coarctation of the aorta and was evaluated for the same with catheter angiography study. Aortograms were taken through both right brachial and femoral routes. Transfemoral catheter failed to pass beyond the proximal descending thoracic aorta, and flush angiograms showing aortic stump are taken. Transbrachial artery catheter angiogram showed abrupt cut off of the arch of aorta distal to the origin of the left subclavian artery. It was interpreted as severe coarctation of aorta and stent dilatation was planned during the same sitting. However even guide wire was not negotiable through the segment and procedure was abandoned. For proper delineation of aortic anatomy, multislice computed tomography (CT) angiography was performed which showed complete discontinuity of lumen of the aorta between the aortic arch and descending thoracic aorta which is separated by an atretic fibrous band of thickness ~3.2 mm suggestive of interruption of the aorta (type A).


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  1. Reardon MJ, Hallman GL, Cooley DA. Interrupted aortic arch: brief review and summary of an eighteen-year experience. Texas Heart Institute Journal. 1984 Sep;11(3):250-259.
  2. Bugan B, Iyisoy A, Celik M, Kucuk U, Boz U, Celik T. Isolated type A interrupted aortic arch in an asymptomatic 19-year-old man. Texas Heart Institute Journal. 2011;38(5):559-561.
  3. Steidele RJ. Samml Chir u Med Beob. Vienna. 1778;2:114.
  4. Gokcebay TM, Batillas J, Pinck RL. Complete interruption of the aorta at the arch. Am J Roentgenol 1972;114:362-370.
  5. Celoria GC, Patton RB. Congenital absence of the aortic arch. American heart journal. 1959 Sep 1;58(3):407-413.
  6. Dillman JR, Yarram SG, D'Amico AR, Hernandez RJ. Interrupted aortic arch: spectrum of MRI findings. American Journal of Roentgenology. 2008 Jun;190(6):1467-1474.
  7. Sakellaridis T, Argiriou M, Panagiotakopoulos V, Krassas A, Argiriou O, Charitos C. Latent congenital defect: interrupted aortic arch in an adult—case report and literature review. Vascular and endovascular surgery. 2010 Jul;44(5):402-406.
  8. John AS, Schaff HV, Drew T, Warnes CA, Ammash N. Adult presentation of interrupted aortic arch: Case presentation and a review of the medical literature. Congenital heart disease. 2011 May;6(3):269-275.
  9. Sato S, Akagi N, Uka M, Kato K, Okumura Y, Kanazawa S. Interruption of the aortic arch: diagnosis with multidetector computed tomography. Japanese journal of radiology. 2011 Jan 1;29(1):46-50.
  10. Vriend JW, Lam J, Mulder BJ. Complete aortic arch obstruction: interruption or aortic coarctation?. The international journal of cardiovascular imaging. 2004 Oct 1;20(5):393-396.
  11. Messner G, Reul GJ, Flamm SD, Gregoric ID, Opfermann UT. Interrupted aortic arch in an adult: single-stage extra-anatomic repair. Texas Heart Institute Journal. 2002;29(2):118-121.
  12. Villalobos MC, De Balderrama DP, y Lopez JL, Castellanos M. Complete interruption of the aorta. American Journal of Cardiology. 1961 Nov 1;8(5):664-669.
  13. Öztürk A, Özcan EE, Özel E, Uyar S, enaslan Ö. Medical treatment of an adult with uncorrected isolated interrupted aorta resulted in no complications after 4 years of follow-up. The American journal of case reports. 2014;15:330-332.
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